Pridopidine Phase 3 Study to Evaluate Efficacy and Safety in ALS

Purpose

The goal of this clinical trial is to learn if the drug pridopidine works to treat amyotrophic lateral sclerosis in adults. It will also help to learn about the safety of pridopidine. The main question it aims to answer is: Does pridopidine slow disease progression of ALS? Researchers will compare pridopidine to a placebo (a look-alike substance that contains no drug) to see if pridopidine works to treat ALS. Participants will: Take pridopidine or a placebo by mouth every day for 48 weeks. Afterwards, all participants will take pridopidine for another 48 weeks. Visit the clinic once every 1-3 months for checkups and tests

Condition

  • Amyotrophic Lateral Sclerosis

Eligibility

Eligible Ages
Between 18 Years and 80 Years
Eligible Sex
All
Accepts Healthy Volunteers
No

Inclusion Criteria

  • Definite ALS or Probable ALS using the El Escorial criteria. - Symptom onset of ≤18 months at screening. - Slow vital capacity (SVC) greater or equal to 60% predicted. - Treatment Research Initiative to Cure ALS (TRICALS) Risk Profile Calculator score, based on the European Network for the Cure of ALS (ENCALS) survival prediction model, in the range of -6 to -2, inclusive, at screening. - Able to swallow a capsule.

Exclusion Criteria

  • Presence of tracheostomy or permanent assisted ventilation. - Clinically significant heart disease, clinically significant history of arrhythmia, symptomatic or uncontrolled atrial fibrillation despite treatment, or asymptomatic sustained ventricular tachycardia, or presence of left bundle branch block. - Presence of unstable psychiatric disease, cognitive impairment, dementia or substance abuse that would impair ability of the participant to provide informed consent and participate in the study. - Clinically significant and/or unstable medical condition (other than ALS) that may either pose a clinically meaningful risk to the participant and/or to study completion. - Use of medications that prolong QT interval. - Previous treatment with pridopidine, gene therapy, or antisense oligonucleotides. - Confirmed mutation in the SOD1, FUS or C9orf72 gene. - Pregnancy.

Study Design

Phase
Phase 3
Study Type
Interventional
Allocation
Randomized
Intervention Model
Parallel Assignment
Intervention Model Description
Randomized (3:2), double-blind, placebo-controlled study followed by an open-label extension period. During the open-label extension, all participants will receive pridopidine.
Primary Purpose
Treatment
Masking
Quadruple (Participant, Care Provider, Investigator, Outcomes Assessor)

Arm Groups

ArmDescriptionAssigned Intervention
Experimental
Pridopidine
Pridopidine hard gelatin capsules of 45 mg strength. During titration period 1 capsule taken orally in the morning for 2 weeks. During the main treatment period, 1 capsule in the morning and 1 capsule in the afternoon taken orally. Total daily dose of 90 mg.
  • Drug: Pridopidine
    Pridopidine hard gelatin capsule.
Placebo Comparator
Placebo
Placebo hard gelatin capsules. During titration period 1 capsule taken orally in the morning for 2 weeks. During the main treatment period, 1 capsule in the morning and 1 capsule in the afternoon taken orally.
  • Drug: Placebo
    Placebo hard gelatin capsule.

Recruiting Locations

Sean M. Healey & AMG Center for ALS
Boston, Massachusetts 02114
Contact:
Julia Stein
617-726-1398
mghpridopidinephase3healey@mgb.org

Somnos Clinical Research
Lincoln, Nebraska 68506
Contact:
402-770-7403
desi@somnos.com

Texas Neurology
Dallas, Texas 75206
Contact:
214-827-3610
sdoyle@texasneurology.com

More Details

NCT ID
NCT07322003
Status
Recruiting
Sponsor
Prilenia

Study Contact

Executive Director Clinical Operations
857-574-5755
MedInfo@prilenia.com

Detailed Description

This is a Phase 3, randomized study consisting of a double-blind placebo-controlled (DBPC) period followed by an open-label extension (OLE) to evaluate the efficacy and safety of pridopidine administered orally at a dose of 45 mg twice a day in adult participants with early and rapidly progressing ALS. Standard of care treatments (e.g. riluzole, edaravone and Nuedexta) will be allowed as long as participants are on a stable dose for at least 4 weeks prior to dosing. In the DBPC period, participants will be randomized in a 3:2 ratio to the pridopidine and placebo arms. In the DBPC period, participants will receive pridopidine or placebo for 48 weeks. In the OLE period, all participants will receive pridopidine for 48 weeks, while maintaining the blind to their original randomization for both the participant as well as the Investigator and other clinical staff. The total study duration per participant will be 102 weeks including screening and follow up. Throughout the study, participants will be assessed through on-site clinic visits and virtual visits (via telephone).